Retroperitoneal paraganglioma

Familial malignant retroperitoneal paraganglioma.

Paragangliomas are neuroendocrine tumours and those occurring in the head and neck have well recognized familial association. Retroperitoneal paragangliomas are uncommon and we present two cases of familial malignant retroperitoneal paraganglioma. Review of the literature revealed marked differences in the incidence and malignant potential of familial and non-familial paraganglioma. In contrast...

Case note: retroperitoneal nonfunctioning paraganglioma.

Paragangliomas are extra-adrenal chromaffin tumours that develop at the expense of neuroectodermal cells of the autonomous nervous system. Retroperitoneal and nonfunctioning forms are very rare. They are often asymptomatic and can reach a substantial size. Treatment usually involves surgery with the goal of total excision. We report the case of a patient who presented with indistinct abdominal ...

Nonfunctional Retroperitoneal Paraganglioma: A Histopathological Surprise

Paragangliomas are the tumors arising from chromaffin tissue which is distributed along the autonomic nervous system. Most of these tumors secrete and store catecholamines. They can be suspected by clinical symptoms and confirmed by biochemical tests. Retroperitoneal paraganglioma mostly arise from adrenal medulla and are also known as adrenal pheochromocytoma. About 10% of abdominal paragangli...

Large retroperitoneal paraganglioma concurrent with periampullary adenocarcinoma

Paragangliomas are tumors that originate from extra-adrenal medullary neural crest derivatives. They are rarely located in retroperitoneal space. These tumors are often discovered incidentally during imaging studies performed for other reasons. Periampullary cancers include adenocarcinomas arising from the pancreas, ampulla of Vater, duodenum or distal common bile duct. The exact site of origin...

Retroperitoneal non-functioning paraganglioma: A case report